蛋白
抗体
检测试剂盒
蛋白MARKER
分子生物学
规格：
查看说明书HADHA Rabbit pAb
Cat#:DPA03158应用：WB,ICC/IF,FC,IP
| Product Name: | HADHA Recombinant Rabbit mAb |
| Cat No.: | RMA01095 |
| Clonality: | Monoclonal |
| Species Reactivity: | Human, Mouse, Rat |
| Tested Applications: | WB,IHC,ICC/IF,FC,IP |
| Recommended Dilution: | WB,IHC,ICC/IF,FC,IP |
| Size: | 30ul 50ul 100uL |
| Format: | Liquid |
| Source: | Rabbit |
| Purification Method: | Affinity Purification |
| Isotype: | IgG |
| Conjugate: | Un-conjugated |
| Storage: | Store at -20°C. Supplied in 50nM Tris-Glycine(pH 7.4), 0.15M NaCl, 40%Glycerol, 0.01% sodium azide a |
| Immunogen: | A synthetic peptide of human HADHA |
| Calculated Molecular Weight: | 83 kDa |
| Observed Molecular Weight: | 78 kDa |
| GenBank Accession Number: | P40939 |
| Gene ID (NCBI): | 3030 |
| Synonyms: | GBP; ECHA; HADH; LCEH; MTPA; LCHAD; TP-ALPHA |
| Background: | This gene encodes the alpha subunit of the mitochondrial trifunctional protein, which catalyzes the last three steps of mitochondrial beta-oxidation of long chain fatty acids. The mitochondrial membrane-bound heterocomplex is composed of four alpha and four beta subunits, with the alpha subunit catalyzing the 3-hydroxyacyl-CoA dehydrogenase and enoyl-CoA hydratase activities. Mutations in this gene result in trifunctional protein deficiency or LCHAD deficiency. The genes of the alpha and beta subunits of the mitochondrial trifunctional protein are located adjacent to each other in the human genome in a head-to-head orientation. [provided by RefSeq, Jul 2008] |
| Category: | Primary Ab |
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